About: Birt–Hogg–Dubé syndrome

An Entity of Type: disease, from Named Graph: http://dbpedia.org, within Data Space: dbpedia.org

Human autosomal dominant genetic disorder that can cause susceptibility to kidney cancer, renal and pulmonary cysts

Property	Value
dbo:description	Krankheit (de) хвороба (uk) مرض يصيب الإنسان (ar) zeldzame ziekte met huidafwijkingen (nl) human autosomal dominant genetic disorder that can cause susceptibility to kidney cancer, renal and pulmonary cysts (en) sindrome ereditaria autosomica dominante legata ad un problema a carico del cromosoma 17 (it) associe des manifestations cutanées, des manifestations pulmonaires à type de kystes et/ ou de pneumothorax et des tumeurs du rein (fr)
dbo:diseasesDB	33274
dbo:eMedicineSubject	derm (en)
dbo:eMedicineTopic	622 (en)
dbo:geneReviewsId	NBK1522
dbo:geneReviewsName	Birt-Hogg-Dubé Syndrome (en)
dbo:omim	135150 (xsd:integer)
dbo:thumbnail	wiki-commons:Special:FilePath/Birt–Hogg–Dubé_syndrome.jpg?width=300
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dbp:align	right (en)
dbp:caption	The characteristic fibrofolliculomas of Birt–Hogg–Dubé syndrome seen on a person's face. (en)
dbp:diseasesdb	33274 (xsd:integer)
dbp:emedicinesubj	derm (en)
dbp:emedicinetopic	622 (xsd:integer)
dbp:footer	Individual with Birt–Hogg–Dubé syndrome, showing the characteristic facial fibrofolliculomas (en)
dbp:genereviewsname	Birt-Hogg-Dubé Syndrome (en)
dbp:genereviewsnbk	NBK1522 (en)
dbp:image	Birt–Hogg–Dubé syndrome2.jpg (en) Birt–Hogg–Dubé syndrome3.jpg (en)
dbp:name	Birt–Hogg–Dubé syndrome (en)
dbp:omim	135150 (xsd:integer)
dbp:onset	adulthood (en)
dbp:width	200 (xsd:integer)
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gold:hypernym	dbr:Disorder
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rdfs:label	Birt–Hogg–Dubé syndrome (en) متلازمة بيرت-هوغ-دوبي (ar) Hornstein-Knickenberg-Syndrom (de) Syndrome de Birt-Hogg-Dubé (fr) Sindrome di Birt-Hogg-Dubé (it) Sindrom Birt–Hogg–Dubé (in) Zespół Birt-Hogg-Dubé (pl) Syndroom van Birt-Hogg-Dubé (nl) Синдром Бёрта — Хога — Дьюба (ru)
rdfs:seeAlso	dbr:List_of_cutaneous_neoplasms_associated_with_systemic_syndromes
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